Idiopathic basal ganglia calcifica- tion (Fahr’s disease) in a 9 - year - old Nigerian child

Abstract

Fahr’s disease is a rare neurodegenerative disorder characterized by deposition of calcium on the walls of blood vessels of the Basal ganglia and Dentate nuclei of the Cerebellum. Patient can present with diverse array of symptoms including but not limited to seizure, extrapyramidal symptoms and mental retardation. We report a case of a 9 year old female child with history of recurrent seizure. Brain CT showed symmetrical calcification in the basal ganglia.

Keywords

• fahr’s syndrome
• intracranial calcification
• seizure