Massive primary pulmonary artery rhabomyosarcoma: A case report

Abstract

Pulmonary artery sarcomas (PAS) are rare tumours causing an insidiously progressive obstruction of the pulmonary circulation. The clinical presentation is often indistinguishable from chronic thromboembolic pulmonary hypertension (CTEPH). However, the atypical appearance of a heterogeneous filling defect in CT pulmonary angiography (CTPA) should prompt further investigation.

Keywords

• pulmonary hypertension
• pulmonary artery
• rhabdomyosarcoma
• endarterectomy
• computed tomography angiography