Type 1 Congenital Pulmonary Airway Malformation (CPAM): A Case Report

Abstract

Congenital Pulmonary Airway Malformation (CPAM) is a lower respiratory tract developmental malformation. It is due to overgrowth of terminal bronchiole causing a dysplastic lesion. Affected areas consist of mass of cysts lined by bronchial or cuboidal epithelium, which may contain cystic and adenomatoid portions with intervening normal lung tissue. We present a rare case of full term female baby with type 1 CPAM, antenatally diagnosed and successfully managed with left lung lower lobe complete lobectomy with maximum cyst size measuring about 5.3x2.3 cm. Histologically cyst resembling bronchioles.

Keywords

• congenital cystic adenomatous malformation
• hamartomatous lesion
• lobectomy
• lung malformation