Large epidural hematoma in a child with progeria syndrome complicated by posterior cerebral artery stroke: A case report

Abstract

Hutchinson-Gilford progeria Syndrome (HGPS) is a genetic disease in which patients manifest with a prematurely aged appearance and cardiovascular disease due to atherosclerosis. A 13-year-old male patient with HGPS was admitted with a history of trauma in the right temporoparietal region of the head, evolving with headache, worsening of previous left hemiparesis and right blepharoptosis. Head tomography showed a large epidural hematoma at the right parieto-occiptal convexity. A craniotomy was performed for drainage of the hematoma. After good evolution, the control tomography showed effective drainage of the hematoma with a new ischemia in the right posterior cerebral artery. In this case possibly the syndrome-related cerebrovascular atherosclerosis contributed to the formation of hematoma and postoperative ischemia.

Keywords

• traumatic brain injury
• epidural hematoma
• hutchison-gilford progeria syndrome