Repair of omphalocele with extensive liver herniation through a small abdominal wall defect by delayed external silo reduction

Abstract

An omphalocele containing the entire liver inside the umbilical cord through a small abdominal wall defect is a rare condition. The surgical management of an omphalocele with extensive liver herniation through a small abdominal wall is extremely challenging due to not only a limited abdominal cavity but also a narrowed umbilical ring. Herein, we report a case of omphalocele with extensive liver herniation through a small abdominal wall treated successfully with a delayed external silo reduction technique, by preserving the amniotic membrane.

Keywords

• Omphalocele
• Delayed reduction
• External silo