Frontiers in Pediatrics (Jun 2022)

Case Report: Primary Thoracic Low-Grade Fibromyxoid Sarcoma in a Young Girl Presenting With Mediastinal Mass Syndrome

  • Yat Chi Chan,
  • Amanda N. C. Kan,
  • Liz Y. P. Yuen,
  • Innes Y. P. Wan,
  • Kevin K. F. Fung,
  • Yiu-fai Cheung,
  • Yiu-fai Cheung,
  • Karen K. Y. Leung,
  • Dennis T. L. Ku,
  • Anthony P. Y. Liu,
  • Anthony P. Y. Liu

DOI
https://doi.org/10.3389/fped.2022.885068
Journal volume & issue
Vol. 10

Abstract

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Low-grade fibromyxoid sarcomas (LGFMSs) are typically adult-onset tumors that arise from the extremities. Here, we report an exceptional case of primary thoracic LGFMS in an 8-year-old girl that resulted in mediastinal syndrome. In reporting this case, we discuss the clinical challenges, role of molecular profiling and review reported cases of pediatric thoracic LGFMSs.

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