Ewing's sarcoma: A rare case report

Abstract

Ewing's sarcoma is an uncommon malignancy, constituting 4%–10% of the entire malignant osseous tumors involving children and young people. Rarely does it affect the facial bones, and added to its nonspecific presentation, its diagnosis remains challenging. Its occurrence is <3% in the head-and-neck region, with the mandible being frequently affected. It belongs to the ES family of tumors, shows rapid growth, and has a greater propensity for metastasis. ES of the jaws either presents as a primary or as a metastatic deposit. We report one such rare clinical and histological scenario of a primary ES of the mandible in a girl, of 8 years of age, whose clinical presentation mimicked that of an odontogenic tumor/cyst. Tumor cells were positive for CD99 and vimentin which confirmed the diagnosis. This report is to showcase the importance of early diagnosis in such rarely occurring aggressive tumors. It further facilitates appropriate therapy to achieve local control, prevent metastasis, and systemic eradication.

Keywords

• ewing's sarcoma
• immunohistochemistry
• mandible