Post- Partum Acute Intermittent Porphyria - A Case Report

Abstract

Porphyrias are inherited disorders, each involving a specific enzyme in heme biosynthetic pathways. Acute intermittent porphyria, one of the hepatic porphyria is the most severe form of the disease, with gastrointestinal and neuropsychiatric manifestations. Proper management will dramatically improve the outcome in this otherwise debilitating and potentially life-threatening disease.

Keywords

• post partum, acute intermittant porphyria,