Dermatofibrosarcoma protuberans at an uncommon site

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a locally aggressive, cutaneous, malignant tumor characterized by high propensity for local relapse and low metastatic potential. It is seen mainly in the age group of 6-65 years over the trunk and extremities. Immunohistochemically it diagnosed by marker human progenitor cell Ag CD 34. Herein, we present a 40-year-old male with DFSP over the pubic area and extending up to the proximal penile shaft. The biopsy revealed intervening bundles of spindle-shaped cells in the dermis and the diagnostic marker human progenitor cell Ag CD 34 was positive. The patient underwent wide local surgical resection.

Keywords

• CD34
• dermatofibrosarcoma protuberans
• soft tissue sarcoma