Development of lymphangioleiomyomatosis in a female patient with Sjö gren's disease: a review of literature and a case report

Abstract

Cystic and bullous lung transformation occurs in diseases of various origins: neoplastic, genetically determined, rheumatic, lymphoproliferative, and infectious diseases. The paper presents a review of the literature and a clinical case of a young female patient with a long history of Sjögren's disease. Fifteen years after the onset of the disease, the patient developed cystic and bullous lung transformation and renal angiomyolipoma, which are regarded as a manifestation of probable lymphangioleiomyomatosis.

Keywords

• sjögren's disease
• sjögren's syndrome
• lymphangioleiomyomatosis
• cystic lung diseases
• clinical case