Revista da Sociedade Portuguesa de Dermatologia e Venereologia (Oct 2023)

Atypical presentation of anti-NXP-2 positive juvenile dermatomyositis

  • Andreia Coimbra-Sousa,
  • Renata Miossi,
  • Fernando H. C. de Souza,
  • Samuel Katsuyuki-Shinjo

Journal volume & issue
Vol. 81, no. 4

Abstract

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Dear Editor, The anti-NXP-2 is one of a myositis-specific autoantibody considered a marker of dermatomyositis (DM)1,2. In addition, there is a strong relationship between NXP-2 autoantibodies and calcinosis, particularly in juvenile DM2.