Double-Outlet Right Atrium – A Rare and Easily Misdiagnosed Entity

Abstract

Double-outlet right atrium (DORA) is a rare clinical entity associated with atrioventricular septal defects. Although it is easily correctable by surgery, it may be misdiagnosed during echocardiographic evaluation. Awareness and a thorough knowledge of this entity, its associations, echocardiographic appearances, surgical techniques, and its embryogenesis can alert the clinician to identify this rare but correctable condition. A young patient with DORA is described in this clinical report.

Keywords

• atrioventricular septal defect
• common atrioventricular valve
• deviated atrial septum
• left superior vena cava
• septum primum