Congenital Segmental Absence of the Bowel Muscle Layer with Duplication of then Bowel in an Adult - An Exceedingly Rare Case Report

Abstract

Congenital segmental absence of bowel muscle layer which is also known as Segmental absence of intestinal musculature (SAIM) is rare cause of obstruction in neonates and exceedingly rare in adults. We present 35 years old male with right iliac fossa (RIF) pain since 7 daysandnot passing stool since 3 days, was operated with suspicion of intestinal tuberculosis (TB). Our case shows two rare anomalies, SAIM and duplication in single patient which makes itunique. Histopathologically it was diagnosed as Congenital segmental absence of bowel muscle layer with duplication of bowel wall.

Keywords

• congenital defect
• duplication of bowel
• segmental absence of intestinal muscle layer
• small intestine