A rare case of incontinentia pigmenti in a male child with dermoscopic and histopathological correlation

Abstract

Incontinentia pigmenti (IP) is a rare X-linked genodermatosis mostly occurring in females with the condition being fatal in males but certain mechanisms may allow survival of male subjects. We report a rare case of IP in a 19-day-old male patient with no history of similar lesions in the family adding to its rarity. The histopathological correlation of the lesions with dermatoscopy showed yellow oil drop-like globular structures correlating with spongiosis in the vesicular stage and verrucous lesions showed brown blotches in a circular pattern with overlying gray-brown dots correlating with hyperkeratosis and dyskeratosis.

Keywords

• dermoscopy
• incontinentia pigmenti
• male