An extremely rare case of classic complete caudal duplication: Dipygus

Abstract

Dipygus is a complete caudal duplication deformity in its severest form. The structures derived from the embryonic cloaca and notochords are duplicated to various extent. We report a male baby who presented to us with complete somatic and visceral duplication below the umbilical level associated with gastroschisis and imperforated anus. Staged surgical corrections were suggested and three out of the four stages were performed successfully.

Keywords

• Axin1 gene
• caudal duplication syndrome
• dipygus
• monocephalus quadripus dibrachius
• WNT pathway