Urethral duplication with rectourethral fistula: Review of two cases

Abstract

Urethral duplication is a very rarely observed congenital anomaly, mostly affecting the males. This case report highlights the management of two patients diagnosed with Type II A, Y-type urethral duplication. An 11-year-old boy was diagnosed with Type II A of Y-type urethral duplication, where the dorsal urethra was completely hypoplastic, and the ventral urethra was communicating with rectum. After the failure of a single-stage inner preputial pedicled tube urethroplasty, a perineoscrotal flap urethroplasty was done, and at present, the patient is waiting for the 2nd stage of surgery. Case 2 is a 14-year-old boy diagnosed with Type II A2, Y-type urethral duplication, where the dorsal urethra at proximal part was hypoplastic with normal caliber of penile urethra, and the ventral urethra was communicating with rectum. The boy was treated with end-to-end urethroplasty, and good surgical outcome was observed. The purpose of this case report is to discuss the management of unusual form of Y-type urethral duplication by staging the surgical procedure.

Keywords

• perineal urethrostomy
• rectourethral fistula
• urethroplasty
• y-type urethral duplication