Case Reports in Dermatology (Jan 2023)

A Rare Case of Prurigo Pigmentosa in a Danish Sibling Couple

  • Maria Danielsen,
  • Kristine Pallesen,
  • Rikke Riber-Hansen,
  • Anne Bregnhøj

DOI
https://doi.org/10.1159/000528422
Journal volume & issue
Vol. 15, no. 1
pp. 26 – 30

Abstract

Read online

Prurigo pigmentosa (PP) is probably underdiagnosed due to lack of awareness. Previously, it was assumed that PP primarily affected Japanese females; however, more cases are reported worldwide, and the pathogenesis is still not completely understood. In this case report, we present two healthy Danish siblings, who developed PP approximately 2 weeks after starting a ketogenic diet, suggesting that both increased levels of ketone bodies in the blood together with a genetic predisposition might play a role in the development of PP.

Keywords