Treatment strategies for OIES complex/cloacal extrophy

Abstract

Cloacal exstrophy is the rarest and most severe form of the exstrophy epispadias complex. Before the 1960s the multiple systemic defects found in association with this anomaly in most cases lead to death of the infant. Developments in surgical technology, neonatal intensive care and antibiotic therapy currently increased the survival rates in the range of 85–90%. Planning for the birth and surgical reconstruction of these patients, the pediatrician, pediatric surgeon and radiologist managing these individuals must beware of the multiple anomalies that coexist with this entity.We present a rare case of a prenatally diagnosed OIES (Omphalocele, Imperforate Anus, Extrophy, Spinal defect) complex born in Bahrain's largest tertiary care center, such rare complicated cases with multiple congenital anomalies need a multidisciplinary team to follow the child as long as he survives.

Keywords

• Cloacal exstrophy
• OEIS complex
• Persistent cloaca