Taquicardia ventricular en miocardiopatía no compactada

Abstract

Introduction: left ventricular noncompaction (LVNC) is a rare disease with genetic origin, characterized by the presence of numerous myocardial trabeculations probably due to a detention of the normal process of the endomyocardial embryogenesis. Clinical case: 33 years-of-age man without pathological history, which had been presented progressive dyspnea, dyspnea at rest and orthopnea since two months ago. At physical examination, the patient had tachypnea, tachycardia, S3 left ventricular gallop and crackles in the bases of the lungs. The electrocardiogram showed sinus tachycardia and unspecified diffuse changes of ST-T. The thoracic radiography displayed cardiomegaly and signs of pulmonary congestion. Color doppler echocardiography revealed left ventricle severely dilated with multiple trabeculations and intertrabecular spaces. Ambulatory electrocardiography for 24 hours reported sinus rhythm, frequent isolated monomorphic ventricular extrasystoles with episode of monomorphic no supported ventricular tachycardia. Conclusion: the clinical manifestations, seriousness and the age of beginning of the symptoms of the LVNC are variable. The differential diagnosis must be done with other common pathologies, especially with hypertrophic cardiomyopathy and dilated cardiomyopathy. Rev.cienc.biomed. 2013;4(2):358-362

Keywords

• Cardiomyopathy dilated; Cardiology; Heart failure; Heart ventricles