Herlyn-Werner-Wunderlich Syndrome with Degenerating Fibroid– Uncommon Presentation of a Rare Anomaly

Abstract

Herlyn-Werner-Wunderlich Syndrome (HWWS) is a rare congenital anomaly of Mullerian and mesonephric ducts characterized by uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. It commonly presents after menarche with symptoms related to obstructive hemivagina. However in patients with significantly normal pubertal and menstrual history, the diagnosis of Mullerian Duct Anomaly (MDA) like HWWS is often missed. Here we report a case of 28 year old primigravida presenting with acute abdomen pain which was followed by spontaneous abortion. This is the first instance of HWWS coexisting with uterine fibroids with/without cystic degeneration based on our literature review. Early and accurate diagnosis for the correct treatment of this entity is also emphasized.

Keywords

• Herlyn-Werner-Wunderlich syndrome
• Mullerian Duct Anomaly
• Spontaneous Abortion