Rupture of a Median Sacral Artery Aneurysm in a Patient with Vascular Ehlers Danlos Syndrome

Abstract

Introduction: Vascular Ehlers Danlos syndrome is a rare connective tissue disease that is associated with various arterial complications. Report: A 25 year old man with vascular Ehlers Danlos syndrome presented with acute lower back pain as a result of a ruptured aneurysm of the median sacral artery (MSA). Prior medical history included several vascular events resulting in a right iliac occlusion. The unusual location of aneurysmal disease of the MSA might be explained by extensive collateral flow recruitment due to this occlusion. Conclusion: Previous vascular events inducing collateral recruitment might justify a more frequent follow up in patients with connective tissue disorders.

Keywords

• Aneurysm
• Connective tissue disease
• Median sacral artery
• Vascular Ehlers Danlos syndrome