Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population

Jue Liu; Jianbo Zhong; Qiaowei  Wang; Yinglian  Cai; Jian  Chen

doi:10.2340/actadv.v103.4806

Acta Dermato-Venereologica (Apr 2023)

Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population

Jue Liu,
Jianbo Zhong,
Qiaowei Wang,
Yinglian Cai,
Jian Chen

Affiliations

Jue Liu: Department of Dermatology, Affiliated Hangzhou First People’s Hospital, Zhejiang University School of Medicine, Hangzhou, China
Jianbo Zhong: Department of Dermatology, Affiliated Hangzhou First People’s Hospital, Zhejiang University School of Medicine, Hangzhou, China
Qiaowei Wang: Department of Dermatology, Yes Skin Care Center, Hangzhou, China
Yinglian Cai: Department of Dermatology, Affiliated Hangzhou First People’s Hospital, Zhejiang University School of Medicine, Hangzhou, China
Jian Chen: Department of Dermatology, Affiliated Hangzhou First People’s Hospital, Zhejiang University School of Medicine, Hangzhou, China

DOI: https://doi.org/10.2340/actadv.v103.4806
Journal volume & issue: Vol. 103

Abstract

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Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare fulminant variant of pityriasis lichenoides et varioliformis acuta (PLEVA) that is characterized by a large ulceronecrotic appearance with high fever and a variety of systemic symptoms. We report here a case of FUMHD in a 17-year-old male Chinese patient who was treated successfully with a combination therapy of methotrexate, methylprednisolone, and intravenous immunoglobulin. In addition, a literature review was conducted to summarize the key characteristics of paediatric FUMHD cases.

Published in Acta Dermato-Venereologica

ISSN: 0001-5555 (Print); 1651-2057 (Online)
Publisher: Medical Journals Sweden
Country of publisher: Sweden
LCC subjects: Medicine: Dermatology
Website: https://medicaljournalssweden.se/actadv

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Abstract

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