PAMJ Clinical Medicine (Dec 2019)

Breast location of Darier and Ferrand dermatofibrosarcoma: a rare case report

  • Karima Mouden,
  • Soukaina Wakrim,
  • Afaf Semmar

DOI
https://doi.org/10.11604/pamj-cm.2019.1.43.21049
Journal volume & issue
Vol. 1, no. 43

Abstract

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Darier and Ferrand Dermatofibrosarcoma (DFS) is a very uncommon pathology type of skin cancer. Breast location remains very rare, with only dozens of cases reported to date in the English literature. We report the case of a 21-year-old woman who presented with a left breast mass that had been present for more than 4 years. Clinical examination found cutaneous mass occupying the upper internal quadrant of the left breast measuring 3 x 2cm. The patient underwent an excision of the mass with positive margin. Histological and immunohistochemical findings were suggestive of a Darier and Ferrand Dermatofibrosarcoma (DFS). In front of this clinical board, wide excision of the mass was performed. 15 months after the end of surgery, the patient was in good health, with excellent local control. The purpose of presenting this case is not only to report an uncommon pathology subtype, but mostly to provide a long-term survival of Darier and Ferrand Dermatofibrosarcoma (DFS) of breast cancer that is very rare.

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