Unilateral pulmonary agenesis and esophageal atresia with a tracheoesphageal fistula-23 year followup

Abstract

Pulmonary agenesis, esophageal atresia and a tracheoesophageal fistula (EA + TEF) are a rare combined congenital anomalies associated with a high morbidity and mortality. For those patients that have survived these malformation, there has been limited long-term follow up. This case report describes a 23-year followup with evaluation of the patient's pulmonary, cardiac and gastrointestinal function.

Keywords

• Congenital pulmonary agenesis
• Esophageal atresia
• Tracheoesophageal fistula