Malignant peripheral nerve sheath tumor of chest wall in a patient with neurofibromatosis: A case report

Abstract

Malignant peripheral nerve sheath tumor is a relatively rare tumor in general population with an incidence of 0.001%. But in patients of Neurofibromatosis the incidence is 2 -5%. It usually affects the extremities in these patients and rarely occurs in other sites like trunk, head and neck, intra spinal region, scalp and Intra cranial regions. We present a case of malignant peripheral nerve sheath tumor of the chest wall in an elderly patient with Neurofibromatosis with review of literature.

Keywords

• malignant peripheral nerve sheath tumor
• neurofibromatosis -1