Perivascular epithelioid cell tumor of the ileum: a case report

Abstract

Perivascular epithelioid cell tumors (PEComa) are tumors of perivascular epithelioid cells with immunohistochemical features of smooth muscle and melanocytic tumors. The PEComa of the gastrointestinal tract is rare. The treatment is surgical, although there are data that suggest a good response to rapamycin.

Keywords

• PEComa
• Immunohistochemistry
• Rapamycin
• Ileum