Primary pulmonary artery sarcoma in the pediatric patient: Review of literature and a case report

Yong Yean Kim, MD, PhD; Tung Thanh Wynn, MD; John David Reith, MD; William B. Slayton, MD; Joanne Lagmay, MD; John Fort, MD; Dhanashree Abhijit Rajderkar, MD

Radiology Case Reports (Jul 2020)

Primary pulmonary artery sarcoma in the pediatric patient: Review of literature and a case report

Yong Yean Kim, MD, PhD,
Tung Thanh Wynn, MD,
John David Reith, MD,
William B. Slayton, MD,
Joanne Lagmay, MD,
John Fort, MD,
Dhanashree Abhijit Rajderkar, MD

Affiliations

Yong Yean Kim, MD, PhD: National Cancer Institute, Pediatric Oncology Branch, 37 Convent Dr, Bethesda, MD 20892, USA; Corresponding author.
Tung Thanh Wynn, MD: University of Florida, Department of Pediatric Hematology/Oncology, Gainesville, FL 32610, USA
John David Reith, MD: Cleveland Clinic, Department of Pathology, Cleveland, OH 44195, USA
William B. Slayton, MD: University of Florida, Department of Pediatric Hematology/Oncology, Gainesville, FL 32610, USA
Joanne Lagmay, MD: University of Florida, Department of Pediatric Hematology/Oncology, Gainesville, FL 32610, USA
John Fort, MD: University of Florida, Department of Pediatric Hematology/Oncology, Gainesville, FL 32610, USA
Dhanashree Abhijit Rajderkar, MD: University of Florida, Department of Pediatric Radiology, Gainesville, FL 32610, USA

Journal volume & issue: Vol. 15, no. 7
pp. 1110 – 1114

Abstract

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Primary pulmonary artery sarcoma (PAS) is extremely rare in children. Nevertheless, distinguishing primary PAS from pulmonary embolism is critical to a child's survival. Primary PAS is commonly misdiagnosed as a pulmonary embolism due to similar presenting symptoms and radiographic findings. However, compared to adults, pulmonary embolism is rare in children, especially in patients who do not have predisposing factors or hypercoagulable state. We present a child with primary PAS which mimicked pulmonary embolism on presentation but eventually was resected and is doing well 5 years after resection. In the absence of predisposing factors or hypercoagulable state, solid tumors such as primary PAS should be considered when assessing a pediatric patient with presumed pulmonary embolism.

Published in Radiology Case Reports

ISSN: 1930-0433 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Medicine (General): Medical physics. Medical radiology. Nuclear medicine
Website: https://www.sciencedirect.com/journal/radiology-case-reports

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