Aborted Sudden Cardiac Death Associated with Short QT Syndrome

Kaoru Okishige, MD; Koji Sugiyama, MD; Minetaka Maeda, MD; Hideshi Aoyagi, MD; Manabu Kurabayashi, MD; Naoto Miyagi, MD; Daisuke Ueshima, MD; Koji Azegami, MD; Tetsuhiro Takei, MD; Toshitaka Itoh, MD; Naomasa Makita, MD

doi:10.1016/S1880-4276(09)80006-9

Journal of Arrhythmia (Jan 2009)

Aborted Sudden Cardiac Death Associated with Short QT Syndrome

Kaoru Okishige, MD,
Koji Sugiyama, MD,
Minetaka Maeda, MD,
Hideshi Aoyagi, MD,
Manabu Kurabayashi, MD,
Naoto Miyagi, MD,
Daisuke Ueshima, MD,
Koji Azegami, MD,
Tetsuhiro Takei, MD,
Toshitaka Itoh, MD,
Naomasa Makita, MD

Affiliations

Kaoru Okishige, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Koji Sugiyama, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Minetaka Maeda, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Hideshi Aoyagi, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Manabu Kurabayashi, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Naoto Miyagi, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Daisuke Ueshima, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Koji Azegami, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Tetsuhiro Takei, MD: Department of Intensive Care Medicine, Nagasaki University, Graduate School of Medicine
Toshitaka Itoh, MD: Heart Center, Yokohama-city Bay Red Cross Hospital
Naomasa Makita, MD: Department of Physiology, Nagasaki University, Graduate School of Medicine

DOI: https://doi.org/10.1016/S1880-4276(09)80006-9
Journal volume & issue: Vol. 25, no. 4
pp. 214 – 218

Abstract

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A 43-year-old male was transferred to our institute. His heart rhythm on admission was ventricular fibrillation (VF) which was successfully defibrillated with a direct current shock (DC). A diagnosis of short QT syndrome (SQTS) was made on the basis of an abnormally short QT interval of 280 ms during the sinus rhythm. During treatment for mild total hypothermia, VF recurred repeatedly necessitating DCs. Nifekalant at a dose of 0.3 mg/kg was intravenously administered, the QT interval was prolonged from 280 to 370 ms and VF no longer recurred. Subsequently the patient underwent implantation of an implantable cardioverter defibrillator.

Published in Journal of Arrhythmia

ISSN: 1880-4276 (Print); 1883-2148 (Online)
Publisher: Wiley
Country of publisher: Australia
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://onlinelibrary.wiley.com/journal/18832148

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Abstract

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