Extraskeletal Ewing’s sarcoma/peripheral primitive neuroectodermal tumor of the small bowel presenting with gastrointestinal perforation

Abstract

Vipul D Yagnik,1 Sushil Dawka21Department of Surgical Gastroenterology, Nishtha surgical hospital and research center, Patan, Gujarat, India; 2Department of surgery, SSR Medical College, Belle Rive, MauritiusAbstract: Extraskeletal Ewing’s sarcoma (E-EWS)/peripheral primitive neuroectodermal tumor (pPNET) is a rare soft tissue tumor that arises from a multipotent progenitor cell and is considered to be of neuroectodermal origin. Although soft tissue E-EWS/pPNETs are common, they are exceedingly rare in the small bowel. Only 30 cases of E-EWS/pPNET of the small bowel have been reported. However, only one case of gastrointestinal perforation has been reported till today. Here, we report the second case of E- EWS/pPNET with gastrointestinal perforation.Keywords: peripheral primitive neuroectodermal tumor, immunohistochemistry, gastrointestinal perforation, surgery, chemotherapy

Keywords

• peripheral primitive neuroectodermal tumor
• Immunohistochemistry
• Gastrointestinal perforation
• Surgery
• Chemotherapy