Thrombotic Thrombocytopenic Purpura in a Patient with Klinefelter Syndrome

Abstract

Thrombotic thrombocytopenic purpura (TTP) is a rare disease associated with microangiopathic hemolytic anemia, thrombocytopenia, fever, neurological disorders, and renal insufficiency pentad. It is a fatal hematologic emergency if left untreated. If plasma exchange is feasible, treatment is easy and comfortable. It should be kept in mind that such as in our patient may be acquired at all congenital illnesses.

Keywords

• Klinefelter syndrome
• thrombotic thrombocytopenic purpura
• plasma exchange