Современная ревматология (Apr 2017)

Long-term follow-up of a female patient with Weber–Christian panniculitis

  • S. F. Akhmerov,
  • T. Yu. Nuriakhmetova,
  • R. Z. Abdrakipov,
  • M. A. Afanasyeva,
  • E. V. Sukhorukova,
  • S. A. Lapshina,
  • R. A. Dzamukov,
  • D. I. Abdulganieva

DOI
https://doi.org/10.14412/1996-7012-2017-2-57-59
Journal volume & issue
Vol. 11, no. 2
pp. 57 – 59

Abstract

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Weber–Christian disease is a rare form of lobular panniculitis characterized by painful subcutaneous nodules on the trunk and limbs commonly concurrent with systemic manifestations and a tendency to relapse. Known are only sporadic cases of a long-term (more than 5-year) followup of patients with Weber–Christian disease. For this reason, there are neither prognostic criteria for the disease no proven conventional treatment option now. The paper describes a clinical case of a female patient with a verified diagnosis of Weber–Christian disease who has a sustained subclinical remission due to low-dose prednisone use and basic antirecurrent therapy.

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