Journal of Cutaneous Immunology and Allergy (Jun 2023)
A case of disseminated extranodal Rosai–Dorfman disease diagnosed by skin manifestations
Abstract
Abstract Rosai–Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969. While classical/nodal RDD is typical, extranodal involvement is seen in up to 43% of all cases, with 23% showing only extranodal lesions. Here, we present a case of disseminated extranodal RDD, where the initial symptoms were cutaneous manifestations.
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