Journal of Cutaneous Immunology and Allergy (Jun 2023)

A case of disseminated extranodal Rosai–Dorfman disease diagnosed by skin manifestations

  • Shintaro Saito,
  • Akihiko Uchiyama,
  • Yayoi Shibusawa,
  • Sei‐ichiro Motegi

DOI
https://doi.org/10.1002/cia2.12286
Journal volume & issue
Vol. 6, no. 3
pp. 105 – 107

Abstract

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Abstract Rosai–Dorfman disease (RDD) is a rare non‐Langerhans cell histiocytosis that was first described as sinus histiocytosis with massive lymphadenopathy by Rosai and Dorfman in 1969. While classical/nodal RDD is typical, extranodal involvement is seen in up to 43% of all cases, with 23% showing only extranodal lesions. Here, we present a case of disseminated extranodal RDD, where the initial symptoms were cutaneous manifestations.

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