Primary Angiosarcoma of the Central Nervous System: Case Report and Review of the Imaging Features

Abstract

Primary angiosarcoma of the central nervous system is a rare malignant tumor with only 28 reported cases so far. Imaging findings have only been reported in a few cases. We report a case of intracranial angiosarcoma in a Caucasian male and present a review of the imaging features in the recent literature. The tumor mostly presents as a well-demarcated, heterogeneous, moderately to strongly enhancing lesion with signs of intratumoral bleeding and surrounding vasogenic edema. The differential imaging features of common hemorrhagic intracranial tumors are discussed.

Keywords

• Angiosarcoma, Primary Angiosarcoma, Primary Central Nervous System (CNS) tumors, Sarcoma