Incidentally Detected Pediatric Case with Absent Right Superior Vena Cava During Transcatheter VSD Closure

Abstract

Persistent left superior vena cava (PLSVC) with an absent right superior vena cava (RSVC) is an extremely rare congenital anomalie in normal atrial situs. Isolated cases are diagnosed incidentally during catheterization. In patients with PLSVC, due to frequent drainage of upper extremity, head and neck veins into coronary sinus, patients with enlarged coronary sinus should be suspected to have absence of the RVCS. In this report, we presented a 7-year-old girl who was diagnosed perimembranous VSD (ventricular septal defect), apparently enlarged coronary sinus, PLSVC with transthoracic echocardiography, and incidentally was recognized absence of RSVC during percutaneouse VSD closure. Consequently, we wanted to draw attention to echocardiographic and angiocardiographic findings of this rare venous anomaly.

Keywords

• Absent right superior vena cava; Amplatzer device; Enlarged coronary sinus; persistent left vena cava; Transcatheter closure