Congenital long-QT Syndrome in a Nigerian child: A Case Report

Abstract

Case report : We describe the clinical manifestation and the challenges of diagnosing Long QT syndrome, type 1 (LQTS1), in an 8-year old girl who presented at the Paediatric Cardiology Clinic with syncopal attacks following dancing and excitement. Her initial ECG showed normal QT interval of 380msec (QTc = 440 msec), but later, increased to 410 msec (QTc = 520 msec) following epinephrine challenge test. Conclusion : The challenges with the diagnosis of LQTS1 in children in resource- constrained setting and the need for vigilance in children with syncopal attacks and other cardiac events with normal QT intervals on an electrocardiogram are thus highlighted.

Keywords

• long-qt
• syncopal attacks
• nigerian child