Frontiers in Immunology (Nov 2011)

Primary Immunodeficiency Diseases: an update on the Classification from the International Union of Immunological Societies Expert Committee for Primary Immunodeficiency

  • Waleed eAl-Herz,
  • Waleed eAl-Herz,
  • Aziz eBousfiha,
  • jean-laurent eCasanova,
  • jean-laurent eCasanova,
  • Helen eChapel,
  • Mary Ellen eConley,
  • Mary Ellen eConley,
  • Charlotte eCunningham-Rundles,
  • Amos eEtzioni,
  • Alain eFischer,
  • Jose Luis Franco,
  • Raif eGeha,
  • Lennart eHammarstrom,
  • Shigeaki eNonoyama,
  • Luigi Daniele Notarangelo,
  • Luigi Daniele Notarangelo,
  • Hans Dieter Ochs,
  • Jennifer ePuck,
  • Chaim M Roifman,
  • Reinhard eSeger,
  • Mimi eTang,
  • Mimi eTang,
  • Mimi eTang

DOI
https://doi.org/10.3389/fimmu.2011.00054
Journal volume & issue
Vol. 2

Abstract

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We report the updated classification of primary immunodeficiency diseases, compiled by the ad-hoc Expert Committee of the International Union of Immunological Societies (IUIS). As compared to the previous edition, more than 15 novel disease entities have been added in the updated version. For each disorders, the key clinical and laboratory features are provided. This updated classification is meant to help in the diagnostic approach to patients with these diseases.

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