Anaesthetic management of a patient with Allgrove syndrome

Abstract

Allgrove syndrome is a rare autosomal recessive disorder, which manifests with adrenal insufficiency, achalasia cardia and alacrimia. Autonomic neuropathy can also be associated with it. Adrenal crisis can be precipitated by surgery, infection or trauma. This disorder poses a challenge to anaesthesiologists during anaesthesia for various surgeries. We report the anaesthetic management of a child with Allgrove syndrome.

Keywords

• Achalasia
• adrenal crisis
• alacrimia
• Allgrove syndrome
• anaesthesia