CLINICAL CASE OF FAMILIAL CARDIOMYOPATHY

Abstract

Cardiomyopathy, according to the definition of the WHO Committee of Experts, is a heterogeneous group of chronic diseases of the heart muscle of unknown etiology, not associated with heart disease, systemic or pulmonary hypertension, congenital or acquired heart defects or metabolic disorders. WHO in 1995 proposed a classification of cardiomyopathies and identified the so-called unclassifiable form (fibroelastosis, etc.). Fibroelastosis is characterized by diffuse proliferation of elastic tissue in the endocardium and subendocardial layers of the myocardium. The etiology is unknown, the hereditary genesis of the disease is assumed. The clinical manifestation of the disease is the first half of life. The course of the disease can be lightning-fast, acute and subacute. The prognosis is unfavorable. This article describes a clinical case of familial cardiomyopathy.

Keywords

• семейная кардиомиопатия
• фиброэластоз