A surgical management of melanotic prognoma tumor of Infancy – A case report

Abstract

Abstract- Melanotic neuroectodermal tumor of infancy (MNTI) is a rare condition that typically presents within the first 6 months of life. It rarely metastasizes but is locally aggressive. Melanotic neuroectodermal tumor of infancy has been reported under several other names including retinal anlage tumor and melanotic progonoma. Most commonly, melanotic neuroectodermal tumor of infancy originates in the maxilla. Tumor in previously reported cases are known to originate from different structures. Recommended treatment of MNTI consists of complete excision with wide tissue margins, although success has been reported after incomplete resection too. For those patients in whom surgical resection is not a preferred option, various chemotherapy approaches have been reported with mixed results ranging from failure to sustained tumor regression. In the present case report we have case of MNTI in one year infant which is successfully treated with subtotal excision.

Keywords

• case report
• Lump in the maxilla
• maxilla tumor
• marginal mandibulectomy
• melanotic neuroectodermal tumor of infancy.