Erythrokeratodermia variabilis: Two case reports

Abstract

Erythrokeratodermia variabilis (EKV) is a rare heterogeneous skin disorder. The classical EKV first described by Mendes da Costa is characterized by two types of skin lesions: (1) figurate hyperkeratotic plaques, and (2) transient erythematous areas. Herein, we report two patients presenting with erythematous and hyperkeratotic lesions that were histopathologically diagnosed with EKV.

Keywords

• Erthyrokeratodermia variabilis
• genodermatosis
• transient erythema