BMC Neurology (Jun 2010)

Spontaneous dural tear leading to intracranial hypotension and tonsillar herniation in Marfan syndrome: a case report

  • Syed Nadir A,
  • Mirza Farhan A,
  • Pabaney Aqueel H,
  • Ahsan Humera

DOI
https://doi.org/10.1186/1471-2377-10-54
Journal volume & issue
Vol. 10, no. 1
p. 54

Abstract

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Abstract Background We describe the case of a 38 year old male with Marfan syndrome who presented with orthostatic headaches and seizures. Case Presentation The patient was diagnosed with Spontaneous Intracranial Hypotension secondary to CSF leaks, objectively demonstrated by MR Myelogram with intrathecal contrast. Epidural autologus blood patch was administered at the leakage site leading to significant improvement. Conclusion Our literature search shows that this is the second reported case of a Marfan patient presenting with symptomatic spontaneous CSF leaks along with tonsillar herniation.