Chronic Thromboembolic Pulmonary Hypertension Secondary to Thrombophilia and Incidentally Diagnosed Atrial Septal Defect

Mehmet Kilinc, MD; Yalin Tolga Yaylali, MD; Bedrettin Yildizeli, MD; Serpil Tas, MD

JACC: Case Reports (Apr 2020)

Chronic Thromboembolic Pulmonary Hypertension Secondary to Thrombophilia and Incidentally Diagnosed Atrial Septal Defect

Mehmet Kilinc, MD,
Yalin Tolga Yaylali, MD,
Bedrettin Yildizeli, MD,
Serpil Tas, MD

Affiliations

Mehmet Kilinc, MD: Department of Cardiology, Ceylanpinar State Hospital, Sanliurfa, Turkey
Yalin Tolga Yaylali, MD: Department of Cardiology, Faculty of Medicine, Pamukkale University, Denizli, Turkey; Address for correspondence: Dr. Yalin Tolga Yaylali, Department of Cardiology, Pamukkale University, Çamlaraltı Mah. Fakulte Cad. No: 13 Kinikli, Denizli 20070, Turkey.
Bedrettin Yildizeli, MD: Department of Thoracic Surgery, School of Medicine, Marmara University, Istanbul, Turkey
Serpil Tas, MD: Department of Cardiovascular Surgery, Kartal Kosuyolu Hospital, University of Health Sciences, Istanbul, Turkey

Journal volume & issue: Vol. 2, no. 4
pp. 658 – 661

Abstract

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A 46-year-old man developed chronic thromboembolic pulmonary hypertension and atrial fibrillation after acute pulmonary embolism. He was found incidentally to have an isolated secundum atrial septal defect, as well as a homozygous mutation for the plasminogen activator inhibitor-1 gene. He was successfully treated with pulmonary endarterectomy and atrial septal defect repair. He has continued to do well on a regimen of dabigatran. (Level of Difficulty: Beginner.)

Published in JACC: Case Reports

ISSN: 2666-0849 (Online)
Publisher: Elsevier
Country of publisher: United States
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the circulatory (Cardiovascular) system
Website: https://www.journals.elsevier.com/jacc-case-reports

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Abstract

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