Indian Dermatology Online Journal (Jan 2020)

Localized grain-leather plaque in urticaria pigmentosa – An unusual coexistence of dual morphology

  • Sanjiv Choudhary,
  • Ankita Srivastava,
  • Deepti Joshi,
  • Santosh Tummudi

DOI
https://doi.org/10.4103/idoj.idoj_540_19
Journal volume & issue
Vol. 11, no. 5
pp. 796 – 798

Abstract

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Urticaria pigmentosa (UP), the most common variant of cutaneous mastocytosis (CM), is characterized by hyperpigmented, brownish macules and patches, with positive Darier's sign. Diffuse cutaneous mastocytosis (DCM), is a rare variant of CM, characterized by diffuse infiltration of the skin by mast cells (MCs), resulting in a typical grain-leather appearance. Blistering is commonly seen in infants with CM but it is not specific for any variant of CM. Herein, we report a case of a 5-month-old male infant who presented with recurrent bullous lesions and hyperpigmented, brownish patches with intervening normal skin suggestive of UP, as well as a single, localized plaque with grain-leather appearance, thereby exhibiting an interesting dual morphology.

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