Bloch Sulzberger syndrome (Incontinentia pigmenti): A rare case report with dental defects

Abstract

Incontinentia Pigmenti (IP) is a multisystem genodermatosis characterized by cutaneous, neurologic, ophthalmologic, and dental abnormalities. This article reports the clinical features and management of a 4-year-old girl diagnosed with IP.

Keywords

• Hypodontia
• incontinentia
• pigmenti
• whorly pigmentation