Pseudopolymorphic Wide Complex Tachycardia in a Child With Long QT Syndrome

Abstract

Implantable loop recorders (ILRs) can be a valuable tool in monitoring patients with inherited arrhythmia. This paper reports on a family with long QT syndrome (type 2 [LQT2]) in which a pseudopolymorphic wide complex tachycardia detected by ILR was ultimately diagnosed as a supraventricular aberrant rhythm, facilitated by noncompliance with beta-blocker therapy. (Level of Difficulty: Intermediate.)

Keywords

• implantable loop recorder
• inherited arrhythmia
• long QT syndrome
• sudden cardiac death
• wide complex tachycardia