Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia

Peter G. Pavlidakey; Alok Mohanty; Lisa J. Kohler; Howard J. Meyerson

doi:10.1155/2011/941637

Case Reports in Hematology (Jan 2011)

Erdheim-Chester Disease Associated with Marginal Zone Lymphoma and Monoclonal Proteinemia

Peter G. Pavlidakey,
Alok Mohanty,
Lisa J. Kohler,
Howard J. Meyerson

Affiliations

Peter G. Pavlidakey: Department of Pathology, University Hospitals Case Medical Center and Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USA
Alok Mohanty: Department of Pathology, University Hospitals Case Medical Center and Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USA
Lisa J. Kohler: Office of the Summit Count Medical Examiner, 85 N. Summit St., Akron, OH 44308-1948, USA
Howard J. Meyerson: Department of Pathology, University Hospitals Case Medical Center and Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106-5056, USA

DOI: https://doi.org/10.1155/2011/941637
Journal volume & issue: Vol. 2011

Abstract

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Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis. We report a fatal case of ECD with extensive cardiac involvement associated with a marginal zone lymphoma and monoclonal proteinemia in a young man. This is the first reported association of ECD with a monoclonal gammopathy or a lymphoma.

Published in Case Reports in Hematology

ISSN: 2090-6560 (Print); 2090-6579 (Online)
Publisher: Wiley
Country of publisher: United Kingdom
LCC subjects: Medicine: Internal medicine: Specialties of internal medicine: Diseases of the blood and blood-forming organs
Website: https://onlinelibrary.wiley.com/journal/3191

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