Unusual right ventricle aneurysm and dysplastic pulmonary valve with mitral valve hypoplasia

Abstract

We report a newborn with an unusual combination of aneurysmally dilated thin-walled right ventricle with hypertrophy of the apical muscles of the right ventricle. There was narrow pulmonary annulus, pulmonary regurgitation, and hypoplasia of the mitral valve and left ventricle. We propose that this heart represents a partial form of Uhl`s anomaly.

Keywords

• Absent pulmonary valve
• right ventricle aneurysm
• Uhl′s anomaly