Surgical treatment of glaucoma associated with the Frank-Kamenetsky’s syndrome (а case report)

Abstract

Purpose. To submit clinical features and the effectiveness of surgical treatment of patients with glaucoma associated with the Frank-Kamenetsky’s syndrome.Material and method. We examined two patients with the Frank-Kamenetsky’s syndrome. Microinvasive non-penetrating deep sclerectomy was performed in both eyes of these patients.Results. The examination of patients detected the following features: x-linked recessive type of inheritance, decreased keratometry parameters with an axial length increase of the eye,specific changes in the anterior segment of the eye: posterior embryotoxon, bluish sclera, unusual iris structure, specific goniodisgenesis and glaucoma starting in adolescence. The combination of these features allowed us to diagnose the Frank-Kamenetsky’s syndrome. The operation and postoperative period were uncompli cated. The intraocular pressure was compensated during the entire follow-up periods.Conclusion. The described clinical cases demonstrate the clinical features of the Frank-Kamenetsky’s syndrome with a specific genetic link. A tolerance to the medical treatment with a fast progression is typical for this type of glaucoma. Surgical treatment allows to compensate the stable hydrodynamic indices ofintraocular pressure, to preserve and improve visual function in these patients.

Keywords

• mesenchymal
• dystrophy
• syndrome
• frank-kamenetsky
• glaucoma
• surgery
• non-penetrating deep sclerectomy