Hematology, Transfusion and Cell Therapy (Oct 2023)
AZERBAIJAN EXPERIENCE OF HAEMOPHILIA CARE
Abstract
Objective: As the management of haemophilia is complex, it is essential that those with the disorder should have ready access to a range of services provided by a multidisciplinary team of specialists. There is a State Program aimed at solving this problem in Azerbaijan. The purpose of the study to learn complex epidemiological characteristics which are necessary for justification of strategy on treatment and prevention of haemophilia. Methodology: For planning of prophylactic treatment in Baku city, there was obtained the database of all patients (by sex, age, diagnosis, severity)registered in the city (625 persons). The main group consisting of 52 patients with severe and 40 patients with moderate haemophilia-A was formed.Different variant treatment of 162 patients was organized in HTC:chemical synovectomy with rifampicin (44); phonophoresis with refined naftalan oil (44); phonophoresis with hydrocortisone (28);electrophoresis with KJ (35). Results: 77.9% of patients observed in treatment and prophylaxis facilities in Baku were men, 59% were diagnosed with haemophilia A, 18.8% with severe and 31.5% with moderate haemophilia.Prophylactic treatment reduces the average annual number of bleeding episodes by 2.2 times in severe haemophilia and 2.1 times in moderate haemophilia. The model of prophylactic treatment of hemophilia can be applied in the infusion model 2 or 3 times a week as far as possible. Conclusion: The role of physiotherapeutic methods of hemarthrosis treatment was assessed and positive results were obtained. Due to the prevalence of polymorbidity in patients with hemophilia the complexity of their observation and treatment and the participation of specialists from several specialties is necessary. As the duration of haemophilia is proportional to the frequency of its complications, starting the prophylactic treatment at the stage when patients are first diagnosed is recommended.