International Medical Case Reports Journal (Feb 2022)
A Rare Case of Dandy-Walker Syndrome
Abstract
Mohammad Sharif Oria,1 Aziz Rahman Rasib,2 Ahmad Fawad Pirzad,3 Fahima Wali Ibrahim Khel,4 Mohammad Ismael Ibrahim Khel,1 Fazel Rahim Wardak5 1Anesthesiology Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan; 2Neuropsychiatry Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan; 3Neurosurgery Department, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan; 4Gynecology and Obstetrics Department, Malalai Maternity Hospital, Kabul, 1003, Afghanistan; 5Microbiology Department, Kabul University of Medical Sciences, Kabul, 1001, AfghanistanCorrespondence: Aziz Rahman Rasib, Department of Neuropsychiatry, Kabul University of Medical Sciences, Kabul, 1001, Afghanistan, Tel +93797089250, Email [email protected]: Dandy-Walker syndrome (DWS) is a rare congenital malformation characterized by hypoplasia of the cerebellar vermis and its upward rotation and cystic enlargement of the fourth ventricle. The clinical manifestations include psychomotor retardation, ataxia and hydrocephalus. We report a case of 16-year-old female patient in Ali Abad Teaching Hospital who was suffering from unsteady gait, memory deterioration and urinary incontinence. A brain magnetic resonance imaging revealed enlarged cystic posterior fossa, dilated fourth ventricles and upward rotated cerebellar vermis which were indicating DWS. The patient prepared for planned surgical operation and a written informed consent was obtained from her parents for surgery and general anesthesia. A cystoperitoneal (CP) shunt was placed and then the patient transferred to recovery room. After recovery and hospital stay, the patient discharged with improved clinical symptoms.Keywords: Dandy Walker syndrome, hydrocephalus, intubation challenge
